Cirrhosis in partial lipodystrophy.
نویسندگان
چکیده
A patient with partial lipodystrophy, fatty liver and cirrhosis, and autoimmune thyroid disease is described. Treatment with thyroxine led to partial improvement in the hepatic abnormality.
منابع مشابه
New advances in the treatment of generalized lipodystrophy: role of metreleptin
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متن کاملA case of Berardinelli-Seip syndrome presenting with cirrhosis.
Berardinelli-Seip congenital lipodystrophy (BSCL) is a rare autosomal recessive disorder of generalised lipoatrophy, characterised by the absence of functioning adipocytes, with lipid being stored in muscles, the liver and the pancreas. The usual presentation is in adulthood, with manifestations of insulin resistance, hypertriglyceridaemia and liver steatosis. Cirrhosis as the first presentatio...
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متن کاملA possible association of partial lipodystrophy with anti-GBM nephritis (Goodpasture's syndrome).
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عنوان ژورنال:
- Postgraduate medical journal
دوره 65 763 شماره
صفحات -
تاریخ انتشار 1989